ABSTRACT
A case of congenital orbital teratoma is described in which there was no organized
eye only microscopic evidence of ocular tissues within the disorganized teratoma.
A baby boy presented at birth with a 10-X-8-cm mass extruding from the left orbit.
Magnetic resonance imaging (MRI) showed a mixed cystic-solid orbital mass containing
areas of calcification and deforming the bony orbit around its margins. There was
no organized eye and no intracranial extension. The eye was removed with reconstruction
of the eyelids. Histopathology showed representation from all three germ cell layers
consistent with a teratoma. There was no organized eye, but some disorganized ocular
structures within the teratoma. Follow-up has been uneventful. Neo-natologists and
pediatricians should be aware of the possible diagnoses in a newborn presenting with
an orbital mass, so that early definitive surgery can be performed with preservation
of the globe where possible.
Keywords
Congenital orbital teratoma
